Syringocistadenocarcinoma papilliferum

Authors

  • Kenia González Valcárcel Hospital Ginecoobstétrico "Mariana Grajales"
  • Eliecer Anoceto Armiñana Hospital Ginecoobstétrico "Mariana Grajales"
  • Irene Carmen Rodríguez Santos Hospital Ginecoobstétrico "Mariana Grajales"
  • María Luisa García Gómez Hospital Ginecoobstétrico "Mariana Grajales"
  • Isdeky Milián Espinosa Hospital Ginecoobstétrico "Mariana Grajales"
  • Yarisleidy Cabrera Abreu Hospital Ginecoobstétrico "Mariana Grajales"
  • María Elena Benavidez Casal Hospital Ginecoobstétrico "Mariana Grajales"
  • Armando Eugenio Iglesias Yera Hospital Ginecoobstétrico Mariana Grajales
  • Doris María Batule Llanes Hospital Ginecoobstétrico Mariana Grajales

Keywords:

tubular sweat gland adenomas, syringocistadenocarcinoma papilliferum, vulva

Abstract

This is a 54-year-old patient who started with an injury to the vulva at the level of the scar of the raffia for about four years, which evolves and abscess, what has been treated several times, without improvement, so it continued with bleeding and pain in the region of the vulva. He decided to go to the Gynecological Consultation of the Mariana Grajales Hospital of Santa Clara, and she was diagnosed with a lesion in the vulvar fork of 3 cm, raised, with indurated and ulcerated edges. The clinical characteristics of the lesion are resolved in the Gynecology Room and a vulvectomy is performed with bilateral inguinal lymphadenectomy. The histological diagnosis consisted of a syringocistadenocarcinoma of the ulcerated infiltrating papillary vulva. Syringocistadenocarcinoma papilliferum is a malignant tumor derived from the sweat glands extremely infrequent. It is located, predominantly, in the head and neck and may develop a papilliferous syringocistadenoma or a sebaceous neva of Jadassohn; Its location in the vulva is uncommon.

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Author Biographies

Kenia González Valcárcel, Hospital Ginecoobstétrico "Mariana Grajales"

Especialista de I Grado en Medicina General Integral y en Anatomía Patológica. Profesora Asistente de la Universidad de Ciencias Médicas de Villa Clara. Investigadora Agregada.

Eliecer Anoceto Armiñana, Hospital Ginecoobstétrico "Mariana Grajales"

Especialista de II Grado en Anatomía Patológica. Profesor Auxiliar de la Universidad de Ciencias Médicas de Villa Clara.

Irene Carmen Rodríguez Santos, Hospital Ginecoobstétrico "Mariana Grajales"

Especialista de II Grado en Anatomía Patológica. Profesora Consultante de la Universidad de Ciencias Médicas de Villa Clara.

María Luisa García Gómez, Hospital Ginecoobstétrico "Mariana Grajales"

Especialista de II Grado en Anatomía Patológica. Profesora Consultante de la Universidad de Ciencias Médicas de Villa Clara.

Isdeky Milián Espinosa, Hospital Ginecoobstétrico "Mariana Grajales"

Especialista de I Grado en Medicina General Integral. Especialista de I Grado en Ginecología y Obstetricia.

Yarisleidy Cabrera Abreu, Hospital Ginecoobstétrico "Mariana Grajales"

Especialista de I Grado en Ginecología y Obstetricia

María Elena Benavidez Casal, Hospital Ginecoobstétrico "Mariana Grajales"

Especialista de I Grado en Ginecología y Obstetricia

Armando Eugenio Iglesias Yera, Hospital Ginecoobstétrico Mariana Grajales

Especialista de I y II Grado en Ginecología y Obstetricia. Profesor Auxiliar de la Universidad de Ciencias Médicas de Villa Clara.

Doris María Batule Llanes, Hospital Ginecoobstétrico Mariana Grajales

Especialista de I Grado en Cirugía General

References

1. Leboit PE, Burg G, Weedon D, Sarasin A, editor. Pathology and Genetics of Skin Tumours. Lyon: IARC Press; 2006.

2. Agulló Pérez AD, Bonaut Iriarte B, Córdoba Iturriagagoitia A, Valcayo Peñalba A. Siringocistadenocarcinoma papilífero, descripción de un caso y revisión de la literatura. Actas Dermo-Sifiliográficas [Internet]. 2018 May [citado 14 Jun 2018];109(4):366-369. Disponible en: https://www.sciencedirect.com/science/article/abs/pii/S0001731017305070

3. Enver Aydin O, Sahin B, Selman Ozkan H, Gore O. Siringocistoadenocarcinoma Papilífero. Dermatol Surg [Internet]. 2011 [citado 14 Jun 2018];37:271-4. Disponible en: http://www.elsevier.es/es-revista-medicina-familia-semergen-40-congresos-38-congreso-nacional-semergen-45-sesion-area-dermatologia-3088-comunicacion-siringocistoadenocarcinoma-papilifero-34283-pdf

4. Arias D, Castellano VM, Córdoba S, Miñano R, Martínez D, Borbujo JM. Siringocistoadenoma papilífero de presentación atípica. Actas Dermosifiliogr [Internet]. 2006 Dic [citado citado 14 Jun 2018];97(10):623-690. Disponible en: http://www.actasdermo.org/es-siringocistoadenoma-papilifero-presentacion-atipica-articulo-13095248

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Published

2019-01-01

How to Cite

1.
González Valcárcel K, Anoceto Armiñana E, Rodríguez Santos IC, García Gómez ML, Milián Espinosa I, Cabrera Abreu Y, et al. Syringocistadenocarcinoma papilliferum. Acta Méd Centro [Internet]. 2019 Jan. 1 [cited 2025 Jul. 1];13(1):130-7. Available from: https://revactamedicacentro.sld.cu/index.php/amc/article/view/1002

Issue

Vol. 13 No. 1 (2019): January-March

Section

Clinicopathological Sessions

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