Anesthetic management of patients with spinocerebellar ataxia type 2. A case report

Authors

Keywords:

spinocerebellar ataxia, anesthetic management, monitoring

Abstract

Introduction: spinocerebellar ataxia type 2 is an autosomal dominant inherited disease in which degeneration of the cerebellum and its afferent and efferent pathways occurs and is characterized by ataxia, dysarthria, dysmetria, adiadochokinesia, action tremor, painful muscle contractures, early neuropathy, nystagmus, pyramidal signs, and cognitive, sleep and autonomic disorders.
Patient information: anesthetic management is reported in a patient in which the main implications of anesthesia are related to neuromuscular degeneration and the possible occurrence of respiratory complications.
Conclusions: the adequate selection of anesthetic agents, the use of non-depolarizing muscle relaxants in reduced doses, epidural anesthesia combined with general anesthesia, early removal of the endotracheal tube or laryngeal mask, early mobilization and neuromuscular and cardiorespiratory monitoring are the fundamental elements in the anesthetic management of this patient.

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Author Biographies

Alina Rodríguez Calderón, Hospital Provincial Clínico Quirúrgico Universitario "Arnaldo Milián Castro"

Especialista de I Grado en Anestesiología y Reanimación. Profesora Asistente en la Universidad de Ciencias Médicas de Villa Clara.

Carlos Gilberto Nieto Monteagudo, Hospital Universitario "Celestino Hernández Robau"

Especialista de I y II Grado en Anestesiología y Reanimación. Profesor Auxiliar en la Universidad de Ciencias Médicas de Villa Clara. Investigador Agregado.

Greter Elena Nieto Martínez, Hospital Provincial Clínico Quirúrgico Universitario "Arnaldo Milián Castro"

Especialista de I Grado en Anestesiología y Reanimación.

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Published

2023-01-05

How to Cite

1.
Rodríguez Calderón A, Nieto Monteagudo CG, Nieto Martínez GE. Anesthetic management of patients with spinocerebellar ataxia type 2. A case report. Acta Méd Centro [Internet]. 2023 Jan. 5 [cited 2025 Jul. 1];17(1):161-7. Available from: https://revactamedicacentro.sld.cu/index.php/amc/article/view/1766

Issue

Vol. 17 No. 1 (2023): January-March

Section

Case Reports

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