Patient with neurofibromatosis type 1 and supratentorial tumor

Authors

  • Isabel González Alemán Hospital Clínico Quirúrgico “Arnaldo Milián Castro”, Santa Clara, Villa Clara, Cuba
  • Agustín Arocha García Hospital Clínico Quirúrgico “Arnaldo Milián Castro”, Santa Clara, Villa Clara, Cuba
  • Isabel C. Marimón Carrazana Hospital Clínico Quirúrgico “Arnaldo Milián Castro”, Santa Clara, Villa Clara, Cuba

Keywords:

neurofibromatosis 1, supratentorial neoplasms/diagnosis

Abstract

The case of a 24-year-old male patient who had a history of neurofibromatosis type 1 and was admitted with headache, vomiting and dysarthria is reported. It was determined the existence of a supratentorial tumor, with a diagnosis of glial tumor of the type diffuse fibrillary astrocytoma grade IV. The report of various tumors associated with Von Recklinghausen's disease, and the imaging and morphological characteristics described, motivated a review the classification of the World Health Organization for tumors of the central nervous system and the classification of St Anne-Mayo for hemispheric tumors, allowing its proper location and its differentiation from other intracranial neoplasms that have been described in patients with the disease. The survival of the patient, for 20 months to date, coincides with the location of the tumor as a slower growing tumor that has undergone an anaplastic transformation, which has a relatively better prognosis.

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Author Biographies

Isabel González Alemán, Hospital Clínico Quirúrgico “Arnaldo Milián Castro”, Santa Clara, Villa Clara, Cuba

Especialista de I y II Grado en Anatomía Patológica. Profesora Auxiliar de la Universidad de Ciencias Médicas de Villa Clara “Dr. Serafín Ruiz de Zárate Ruiz”.

Agustín Arocha García, Hospital Clínico Quirúrgico “Arnaldo Milián Castro”, Santa Clara, Villa Clara, Cuba

Especialista de I Grado en Neurocirugía. Profesor Asistente de la Universidad de Ciencias Médicas de Villa Clara “Dr. Serafín Ruiz de Zárate Ruiz”.

Isabel C. Marimón Carrazana, Hospital Clínico Quirúrgico “Arnaldo Milián Castro”, Santa Clara, Villa Clara, Cuba

Especialista de I Grado en Radiología. Profesor Asistente de la Universidad de Ciencias Médicas de Villa Clara “Dr. Serafín Ruiz de Zárate Ruiz”.

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How to Cite

1.
González Alemán I, Arocha García A, Marimón Carrazana IC. Patient with neurofibromatosis type 1 and supratentorial tumor. Acta Méd Centro [Internet]. 2012 Jul. 13 [cited 2025 Jul. 15];6(3):64-70. Available from: https://revactamedicacentro.sld.cu/index.php/amc/article/view/746

Issue

Vol. 6 No. 3 (2012): July-September

Section

Case Reports

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