Uterine perivascular epithelial cell tumor (PEComa), a rare tumor
Keywords:
perivascular epithelioid cell neoplasms, uterusAbstract
A female patient of 47 year olds, of white race, with a history of being deaf-mute and mentally retarded as well as having type 2 diabetes mellitus and essential hypertension for which she is being treated. On this occasion she went to her health area due to vaginal bleeding of six months of evolution; Performed a physical examination and gynecological ultrasound and were diagnosed with a uterine fibroma, so she was referred to the Gynecological Obstetrical Hospital “Mariana Grajales” to undergo surgery. In the surgical act the removal of the cervix was difficult; Was received in several fragments. The anatomopathological study reported the presence in the cervix of a perivascular epithelial cell tumor (PEComa). PEComas are a family of tumors of mesenchymal origin with similar cytomorphological and immunohistochemical characteristics due to the presence of epithelioid and fusocellular cells with eosinophilic or clear cytoplasm that are closely related to the vasculature and characteristically co-express melanocytic and myoid markers. They are extremely rare tumors that, due to their perivascular disposition, can be located in any part of the body (in the literature they are described in diverse parts of the organism), as well as to affect any age or sex; although it draws attention its greater predisposition towards the female sex.Downloads
References
1. Kurman R, Hedrick L, Ronnett B. Blausteins pathology of the female genital tract [Internet]. 6th ed. New York: Springer; 2011[citado 17 Ene 2017]. Disponible en: http://www.springer.com/us/book/9781441904881
2. Christopher F, Krishnan K, Mertens F. World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of Soft Tissue and Bone [Internet]. Lyon, France: IART Prees; 2002 [citado 17 Ene 2017]. Disponible en: https://www.iarc.fr/en/publications/pdfs-online/pat-gen/bb5/BB5.pdf
3. Rosai J. Rosai and Ackermans Surgical pathology [Internet]. 10th ed. New York: Mosby; 2011 [citado 17 Ene 2017]. Disponible en: https://www.elsevier.com/books/rosai-and-ackermans-surgical-pathology-2-volume-set/rosai/978-0-323-06969-4
4. Nucci MR. Foundation in Gynecologic pathology [Internet]. Boston: Elsevier; 2009 [citado 17 Ene 2017]. Disponible en: https://elsevier.ca/product.jsp?isbn=9780443069208
5. Weidner N, Dabbs DJ, Peterson M. Female reproductive system. En: Weidener N, Cote RI, Suster S, Weiss LM. Modern Sugical Pathology. 2nd ed. Philadelphia: Saunders - Elsevier; 2009. p. 1330.
6. Cuevas Herreros Ó, Escobar Lezcano L, Rodríguez Blaco M, Artigas Raventós V. PEComa, un raro tumor de células epiteloides. Rev Esp Cir [Internet]. 2015 Ago [citado 17 Ene 2017]; 93(7): [aprox. 5 p.]. Disponible en: http://www.elsevier.es/es-revista-cirugia-espanola-36-articulo-pecoma-un-raro-tumor-celulas-S0009739X13002571
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15 junio 2025
