Inter-aorto-cava retroperitoneal paraganglioma. Case Report

Authors

Keywords:

retroperitoneal paraganglioma, inter aorto cava

Abstract

Introduction: paragangliomas are very rare extra-adrenal tumors originating from the autonomic nervous system. They are classified in functioning or non-functioning tumors, according to the production of catecholamines.
Patient information: 40-year-old woman, with a history of severe arterial hypertension, who had been treated with three hypotensive drugs without obtaining control; she began to suffer diffuse abdominal pain that increased, associated with hyperpolymenorrhea and a periumbilical tumor of approximately 8 cm, painful and mobile. Laboratory tests were normal. Computed tomography and magnetic resonance imaging confirmed the diagnosis of an 8×5 cm retroperitoneal tumor attached to the aorta and displacing the inferior cava. It was necessary to carry out a highly complex surgical intervention. A tumor was found and the histological and immunohistochemical results confirmed the existence of a non-functioning extra-adrenal paraganglioma.
Conclusions: retroperitoneal paraganglioma is a rare tumor, as shown by statistics. The diagnosis was made, fundamentally, by imaging, histological and immunohistochemical studies. Treatment is fundamentally surgical, as was performed in this patient.

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Author Biographies

Pedro León Acosta, Hospital Provincial Clínico Quirúrgico Universitario “Manuel Ascunce Domenech”

Especialista en II Grado en Medicina Interna. Especialista en II Grado en Medicina Intensiva y Emergencias. Profesor Asistente en la Universidad de Ciencias Médicas de Camagüey. Investigador Agregado.

Pedro Rosales Torres, Hospital Provincial Clínico Quirúrgico Universitario “Manuel Ascunce Domenech”

Especialista en I Grado en Anatomía Patológica. Profesor Instructor en la Universidad de Ciencias Médicas de Camagüey.

Rafael Pila Pérez, Hospital Provincial Clínico Quirúrgico Universitario “Manuel Ascunce Domenech”

Especialista en I y II Grado en Medicina Interna. Profesor Titular y Consultante en la Universidad de Ciencias Médicas de Camagüey.

Rafael Pila Peláez, Hospital Provincial Clínico Quirúrgico Universitario “Manuel Ascunce Domenech”

Especialista en I y II Grado en Medicina Interna. Profesor Auxiliar en la Universidad de Ciencias Médicas de Camagüey.

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Published

2022-01-19

How to Cite

1.
León Acosta P, Rosales Torres P, Pila Pérez R, Pila Peláez R. Inter-aorto-cava retroperitoneal paraganglioma. Case Report. Acta Méd Centro [Internet]. 2022 Jan. 19 [cited 2025 Jul. 2];16(1):165-71. Available from: https://revactamedicacentro.sld.cu/index.php/amc/article/view/1622

Issue

Vol. 16 No. 1 (2022): January-March

Section

Case Reports

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