Cryptogenic organizational pneumonia

Authors

  • Clara García Enríquez Hospital Clínico Quirúrgico Arnaldo Milián Castro
  • Naudica Philip Hospital Clínico Quirúrgico Arnaldo Milián Castro
  • Luis Alberto Santos Pérez Hospital Clínico Quirúrgico Arnaldo Milián Castro
  • Eduardo Gerardo Fernández Ruiz Hospital Clínico Quirúrgico Arnaldo Milián Castro
  • Yoel Santos Treto Hospital Clínico Quirúrgico Arnaldo Milián Castro
  • Alberto Jesús Olivera Echavarría Hospital Clínico Quirúrgico Arnaldo Milián Castro
  • Alejandro Eduardo Gutiérrez Hernández Hospital Clínico Quirúrgico Arnaldo Milián Castro
  • Edelkis Mederos Muro Hospital Clínico Quirúrgico Arnaldo Milián Castro
  • Yolanda del Carmen Inampué Fuelantala Hospital Clínico Quirúrgico Arnaldo Milián Castro
  • Maikel Carballo Fernández Hospital Clínico Quirúrgico Arnaldo Milián Castro
  • Halbert Hernández Negrín Hospital Clínico Quirúrgico Arnaldo Milián Castro http://orcid.org/0000-0002-9992-9148

Keywords:

cryptogenic organizing pneumonia, lung diseases interstitial

Abstract

Male patient of 74 years old, with personal pathological histories of obesity, hypertension, diabetes mellitus and left branch block of the bundle of His. He began with dyspnea and dry cough that did not improve with the treatment imposed by the family doctor. He went to the Cardiocentro “Ernesto Che Guevara” and carried out complementary tests: hemoglobin (low figures), creatinine and uric acid (elevated), from where he was referred to “Arnaldo Milián Castro” Hospital Guardhouse: bibasal crackles were heard in the respiratory system, systolic murmur II/VI in aortic and pulmonary focus and edema of the lower limbs; a chest x-ray showed cottony speckling on both lung bases and an echocardiogram signs of severe pulmonary hypertension. He was admitted with diagnoses of chronic kidney disease due to diabetic nephropathy and arterial hypertension; he evolved poorly, he did not respond to the treatments and died of respiratory failure 18 days after admission. The findings at necropsy allowed the diagnosis of decompensated chronic cor pulmonale in a patient suffering from severe pulmonary hypertension due to cryptogenic organizing pneumonia as a basic cause of death.

Downloads

Download data is not yet available.

Author Biographies

Clara García Enríquez, Hospital Clínico Quirúrgico Arnaldo Milián Castro

Especialista de II Grado en Anatomía Patológica. Profesora Auxiliar de la Universidad de Ciencias Médicas de Villa Clara.

Naudica Philip, Hospital Clínico Quirúrgico Arnaldo Milián Castro

Residente de Anatomía Patológica

Luis Alberto Santos Pérez, Hospital Clínico Quirúrgico Arnaldo Milián Castro

Especialista de I Grado en Medicina Interna. Especialista de II Grado en Medicina Intensiva. Máster en Medicina Intensiva y Eemergencias. Máster en Enfermedades Infecciosas. Profesor Auxiliar y Consultante de la Universidad de Ciencias Médicas de Villa Clara.

Eduardo Gerardo Fernández Ruiz, Hospital Clínico Quirúrgico Arnaldo Milián Castro

Especialista de I Grado en Medicina Interna. Especialista de II Grado en Nefrología. Máster en Urgencias Médicas. Profesor Auxiliar de la Universidad de Ciencias Médicas de Villa Clara.

Yoel Santos Treto, Hospital Clínico Quirúrgico Arnaldo Milián Castro

Especialista de I Grado en Medicina General Integral y en Nefrología. Máster en Educación Médica. Profesor Asistente de la Universidad de Ciencias Médicas de Villa Clara.

Alberto Jesús Olivera Echavarría, Hospital Clínico Quirúrgico Arnaldo Milián Castro

Residente de Nefrología

Alejandro Eduardo Gutiérrez Hernández, Hospital Clínico Quirúrgico Arnaldo Milián Castro

Residente de Nefrología

Edelkis Mederos Muro, Hospital Clínico Quirúrgico Arnaldo Milián Castro

Residente de Medicina Interna

Yolanda del Carmen Inampué Fuelantala, Hospital Clínico Quirúrgico Arnaldo Milián Castro

Residente de Medicina Interna

Maikel Carballo Fernández, Hospital Clínico Quirúrgico Arnaldo Milián Castro

Residente de Geriatría

Halbert Hernández Negrín, Hospital Clínico Quirúrgico Arnaldo Milián Castro

Residente de Medicina Interna

References

1. Fukuoka J. Chronic Diffuse Lung Diseases. En: Leslie KO, Wick MR. Practical pulmonary pathology: a diagnostic approach Philadelphia, PA: Elsevier; 2011. p. 213-225.

2. Corrin B, Nicholson AG. Alveolar filling defects. En: Pathology of lungs chapter. 3ra ed. London: Churchill Livingstone; 2011 p. 308-311.

3. Kumar V, Abbas AK, Fausto N, Aster JC. Robbins y Cotran Patología estructural y funcional. 8va ed. España: Elsevier; 2010.

4. Simonneau G, Galie N, Rubin LJ. Clinical classification of pulmonary hypertension. J Am Coll Cardiol. 2004 Jun 16;43 (12 Suppl S):5S-12S.

5. Montani D, Achouh L, Dorfmuller P. Pulmonary veno occlusive disease: clinical, functional, radiologic, and hemodynamic characteristics and outcome of 24 cases confirmed by histology. Medicine (Baltimore). 2008 Jul;87(4):220-33. doi: 10.1097/MD.0b013e31818193bb.

6. Dorfmuller P, Humbert M, Perros F. Fibrous remodeling of the pulmonary venous system in pulmonary arterial hypertension associated with connective tissue diseases. Hum Pathol. 2007 Jun;38(6):893-902. Epub 2007 Mar 21.

7. Wright JL, Levy RD, Churg A. Pulmonary hypertension in chronic obstructive pulmonary disease: current theories of pathogenesis and their implications for treatment. Thorax [Internet]. 2005 Jul [citado 10 Sept];60(7):605-9. Disponible en: https://www.ncbi.nlm.nih.gov/pubmed/15994270

8. Shorr AF, Wainright JL, Cors CS. Pulmonary hypertension in patients with pulmonary fibrosis awaiting lung transplant. Eur Respir J. 2007 Oct;30(4):715-21. Epub 2007 Jul 11.

9. Badesch DB, Abman SH, Simonneau G. Medical therapy for pulmonary arterial hypertension: updated ACCP evidence based clinical practice guidelines. Chest [Internet]. 2007 Jun [citado 10 Sept];131(6):1917–1928. Disponible en: https://www.ncbi.nlm.nih.gov/pubmed/17565025

10. Humbert M, Sitbon O, Simonneau G. Treatment of pulmonary arterial hypertension. N Engl J Med [Internet]. 2004 Sep 30 [citado 10 Sept];351(14):1425-36. Disponible en: https://www.ncbi.nlm.nih.gov/pubmed/15459304

Published

2018-01-01

How to Cite

1.
García Enríquez C, Philip N, Santos Pérez LA, Fernández Ruiz EG, Santos Treto Y, Olivera Echavarría AJ, et al. Cryptogenic organizational pneumonia. Acta Méd Centro [Internet]. 2018 Jan. 1 [cited 2025 Jul. 2];12(1):104-23. Available from: https://revactamedicacentro.sld.cu/index.php/amc/article/view/883

Issue

Section

Clinicopathological Sessions