Vaginoplasty through Mayer technique in Rokitansky-Hauser-Kuster Syndrome. Apropos of a case

Authors

  • Pedro Borges Echevarría Hospital Ginecoobstétrico “Mariana Grajales”, Santa Clara, Villa Clara, Cuba
  • Serafín Palma Mora Hospital Ginecoobstétrico “Mariana Grajales”, Santa Clara, Villa Clara, Cuba
  • Nuria Vega Betancourt Hospital Ginecoobstétrico “Mariana Grajales”, Santa Clara, Villa Clara, Cuba

Keywords:

congenital abnormalities/etiology, mullerian ducts, gynecologic surgical procedures

Abstract

The Rokitansky-Hauser-Kuster Syndrome is a serious congenital abnormality of the female reproductive tract. It has an embryologic etiology by a failure of fusion of the mullerian ducts. It may coincide with other kidney and skeletal malformations, mainly of the spine and ribs, and others in the abdominal cavity. The karyotype is 46xx, therefore, the patient may or may not have uterus, fallopian tubes, ovaries, normal hair distribution, or may also present agenesis of the genital organs. There is a familial appearance and an autosomal dominant mutation linked to sex. Its diagnosis is presumptive in childhood and adolescence. The clinical, diagnostic and therapeutic characteristics of a patient with vaginal agenesis are presented, as well as the creation of an artificial vagina.

Downloads

Download data is not yet available.

Author Biographies

Pedro Borges Echevarría, Hospital Ginecoobstétrico “Mariana Grajales”, Santa Clara, Villa Clara, Cuba

Especialista de I Grado en Ginecología y Obstetricia. Profesor Asistente de la Universidad de Ciencias Médicas de Villa Clara “Dr. Serafín Ruiz de Zárate Ruiz”.

Serafín Palma Mora, Hospital Ginecoobstétrico “Mariana Grajales”, Santa Clara, Villa Clara, Cuba

Especialista de I y II Grado en Ginecología y Obstetricia. Máster en Medicina Natural y Tradicional. Profesor Asistente de la Universidad de Ciencias Médicas de Villa Clara “Dr. Serafín Ruiz de Zárate Ruiz”.

Nuria Vega Betancourt, Hospital Ginecoobstétrico “Mariana Grajales”, Santa Clara, Villa Clara, Cuba

Especialista de I Grado en Ginecología y Obstetricia. Máster en Atención Integral a la Mujer. Profesor Asistente de la Universidad de Ciencias Médicas de Villa Clara “Dr. Serafín Ruiz de Zárate Ruiz”.

Downloads

How to Cite

1.
Borges Echevarría P, Palma Mora S, Vega Betancourt N. Vaginoplasty through Mayer technique in Rokitansky-Hauser-Kuster Syndrome. Apropos of a case. Acta Méd Centro [Internet]. 2011 Jan. 13 [cited 2025 Jul. 14];5(1):38-43. Available from: https://revactamedicacentro.sld.cu/index.php/amc/article/view/549

Issue

Vol. 5 No. 1 (2011): January-March. Special Issue of Obstetrics and Gynecology

Section

Case Reports

License

Authors who have publications with this journal agree to the following terms:

  1. Authors will retain their copyright and assign to the journal the right of first publication of their work, which will simultaneously be subject to a Creative Commons License / Attribution-Noncommercial 4.0 International (CC BY-NC 4.0) that allows third parties to share the work as long as its author and first publication in this journal are indicated.
  2. Authors may adopt other non-exclusive license agreements for distribution of the published version of the work (e.g., depositing it in an institutional repository or publishing it in a monographic volume) as long as the initial publication in this journal is indicated.
  3. Authors are allowed and encouraged to disseminate their work through the Internet (e.g., in institutional telematic archives or on their web page) before and during the submission process, which can produce interesting exchanges and increase citations of the published work. (See The effect of open access).